Inherited epidermolysis bullosa (EB) is a family of rare genetic skin disorders characterized by structural and mechanical fragility of skin and mucosal membranes. The main feature of EB is the presence of recurrent skin blistering or erosions, which have a profound impact in the quality of life of EB patients and, in the most severe forms, cause early lethality. During the past two decades, it became possible to identify mutations in genes responsible for different types of EB and characterize the abnormalities of the related proteins. Nowadays, there is no cure for EB; all the treatments are palliative and focused on the relief of the devastating EB clinical picture. Recent advancements in molecular biology, stem cell biology and regenerative medicine have fostered new therapeutic approaches for EB. This review is focused on recent developments in gene therapy, protein replacement and cell-based therapy for EB, all aimed at finding a cure for this devastating disease.

The long and winding road that leads to a cure for epidermolysis bullosa / Carulli, Sonia; Contin, Roberta; DE ROSA, Laura; Pellegrini, Graziella; DE LUCA, Michele. - In: REGENERATIVE MEDICINE. - ISSN 1746-0751. - STAMPA. - 8:4(2013), pp. 467-481. [10.2217/rme.13.33]

The long and winding road that leads to a cure for epidermolysis bullosa

CARULLI, SONIA;CONTIN, ROBERTA;DE ROSA, LAURA;PELLEGRINI, Graziella;DE LUCA, Michele
2013

Abstract

Inherited epidermolysis bullosa (EB) is a family of rare genetic skin disorders characterized by structural and mechanical fragility of skin and mucosal membranes. The main feature of EB is the presence of recurrent skin blistering or erosions, which have a profound impact in the quality of life of EB patients and, in the most severe forms, cause early lethality. During the past two decades, it became possible to identify mutations in genes responsible for different types of EB and characterize the abnormalities of the related proteins. Nowadays, there is no cure for EB; all the treatments are palliative and focused on the relief of the devastating EB clinical picture. Recent advancements in molecular biology, stem cell biology and regenerative medicine have fostered new therapeutic approaches for EB. This review is focused on recent developments in gene therapy, protein replacement and cell-based therapy for EB, all aimed at finding a cure for this devastating disease.
2013
8
4
467
481
The long and winding road that leads to a cure for epidermolysis bullosa / Carulli, Sonia; Contin, Roberta; DE ROSA, Laura; Pellegrini, Graziella; DE LUCA, Michele. - In: REGENERATIVE MEDICINE. - ISSN 1746-0751. - STAMPA. - 8:4(2013), pp. 467-481. [10.2217/rme.13.33]
Carulli, Sonia; Contin, Roberta; DE ROSA, Laura; Pellegrini, Graziella; DE LUCA, Michele
File in questo prodotto:
File Dimensione Formato  
rme.13.33.pdf

Accesso riservato

Tipologia: Versione pubblicata dall'editore
Dimensione 971.11 kB
Formato Adobe PDF
971.11 kB Adobe PDF   Visualizza/Apri   Richiedi una copia
Pubblicazioni consigliate

Licenza Creative Commons
I metadati presenti in IRIS UNIMORE sono rilasciati con licenza Creative Commons CC0 1.0 Universal, mentre i file delle pubblicazioni sono rilasciati con licenza Attribuzione 4.0 Internazionale (CC BY 4.0), salvo diversa indicazione.
In caso di violazione di copyright, contattare Supporto Iris

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11380/963721
Citazioni
  • ???jsp.display-item.citation.pmc??? 4
  • Scopus 21
  • ???jsp.display-item.citation.isi??? 18
social impact