Kienböck Disease in a patient with systemic sclerosis: a case report.

Kienböck's disease (KD), described by Robert Kienböck in 1910, is a rare disease characterized by osteonecrosis of the carpal lunate bone. The dominant hand of males in adulthood is predominantly affected, with peak of incidence between the second and fourth decade. The KD is rarely bilateral; early diagnosis is based on MRI or CT findings. The etiology of KD is uncertain, but the theory of repeated traumatism/microtraumatism associated with vascular changes is considered to be a reliable hypothesis. We describe the rare case of a patient followed in our Rheumatology Unit affected by systemic sclerosis (SSc) since 1996 and recently complicated by KD.