Acute intermittent porphyria (AIP) is a disorder of the heme biosynthesis pathway of a specific inherited enzymatic defect. Many different environmental factors such as drugs, calorie restriction, infection etc., often play a key role in triggering a porphiric acute attack. We describe a 50-year-old woman with AIP who underwent aortic valve replacement due to acute infective endocarditis and review the perioperative management of these patients. © 2011 Wiley Periodicals, Inc.

Cardiac surgery in patients with acute intermittent porphyria / Benassi, Filippo; Righi, Elena; Cimato, Paolo; Parravicini, Roberto. - In: JOURNAL OF CARDIAC SURGERY. - ISSN 0886-0440. - 27:(2012), pp. 331-334. [10.1111/j.1540-8191.2011.01350.x]

Cardiac surgery in patients with acute intermittent porphyria

BENASSI, Filippo;PARRAVICINI, Roberto
2012

Abstract

Acute intermittent porphyria (AIP) is a disorder of the heme biosynthesis pathway of a specific inherited enzymatic defect. Many different environmental factors such as drugs, calorie restriction, infection etc., often play a key role in triggering a porphiric acute attack. We describe a 50-year-old woman with AIP who underwent aortic valve replacement due to acute infective endocarditis and review the perioperative management of these patients. © 2011 Wiley Periodicals, Inc.
2012
27
331
334
Cardiac surgery in patients with acute intermittent porphyria / Benassi, Filippo; Righi, Elena; Cimato, Paolo; Parravicini, Roberto. - In: JOURNAL OF CARDIAC SURGERY. - ISSN 0886-0440. - 27:(2012), pp. 331-334. [10.1111/j.1540-8191.2011.01350.x]
Benassi, Filippo; Righi, Elena; Cimato, Paolo; Parravicini, Roberto
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11380/1085429
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