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Characterization of the R7S mutation of Heat Shock Protein HSPB3 and of two novel mutations found in patients suffering of myopathy: understanding the mechanisms leading to disease. 1-gen-2013 Heldens, Lonneke; Morelli, FEDERICA FRANCESCA; Verbeek, Dineke; Vinet, Jonathan; Angelini, Corrado; Boelens, Wilbert; Tupler, Rossella; Carra, Serena
BAG3 induces the sequestration of proteasomal clients into cytoplasmic puncta: implications for a proteasome-to-autophagy switch 1-gen-2014 Minoia, Melania; Boncoraglio, Alessandra; Vinet, Jonathan; Morelli, FEDERICA FRANCESCA; Brunsting, Jeanette F; Poletti, Angelo; Krom, Sabine; Reits, Eric; Kampinga, Harm H; Carra, Serena
Inhibition of autophagy, lysosome and VCP function impairs stress granule assembly 1-gen-2014 Seguin, SAMUEL JOSEPH ANDRE'; Morelli, FEDERICA FRANCESCA; Vinet, Jonathan; Amore, D; DE BIASI, Sara; Poletti, A; Rubinsztein, Dc; Carra, Serena
CHARACTERIZATION OF THE R7S MUTATION OF HEAT SHOCK PROTEIN HSPB3 AND TWO NOVEL MUTATIONS FOUND IN PATIENTS SUFFERING OF MYOPATHY: UNDERSTANDING THE MECHANISMS LEADING TO DISEASE. 1-gen-2015 Morelli, FEDERICA FRANCESCA; Heldens, Lonneke; Verbeek, Dineke; Angelini, Corrado; Cenacchi, Giovanna; Tupler, Rossella; Carra, Serena
OVEREXPRESSION OF HSPB8 PROTECTS AGAINST TDP43-MEDIATED TOXICITY IN DROSOPHILA 1-gen-2015 Ganassi, Massimo; Diacci, Chiara; Seguin, SAMUEL JOSEPH ANDRE'; Zelotti, Elena; Morelli, FEDERICA FRANCESCA; Crippa, Valeria; Poletti, Angelo; Gregory, Jenna M; Dobson, Christopher M; Pandey, Udai B; Carra, Serena
VCP AND AUTOPHAGOLYSOSOMAL PATHWAY: GUARDIANS OF PROTEOSTASIS AND STRESS GRANULE DYNAMICS. UNRAVELING THEIR IMPLICATIONS IN ALS 1-gen-2015 Ganassi, Massimo; Bigi, Ilaria; Seguin, SAMUEL JOSEPH ANDRE'; Morelli, FEDERICA FRANCESCA; Mandrioli, J; Cereda, C; Poletti, A; Carra, Serena
Characterization of the R7S mutation of Heat Shock Protein HSPB3 and of two novel mutations found in patients suffering of myopathy: understanding the mechanisms leading to disease. 1-gen-2015 Morelli, FEDERICA FRANCESCA; Heldens, Lonneke; Verbeek, Dineke; Angelini, Corrado; Cenacchi, Giovanna; Tupler, Rossella; Carra, Serena
A Surveillance Function of the HSPB8-BAG3-HSP70 Chaperone Complex Ensures Stress Granule Integrity and Dynamism 1-gen-2016 Ganassi, Massimo; Mateju, Daniel; Bigi, Ilaria; Mediani, Laura; Poser, Ina; Lee, Hyun O.; Seguin, SAMUEL JOSEPH ANDRE'; Morelli, FEDERICA FRANCESCA; Vinet, Jonathan; Leo, Giuseppina; Pansarasa, Orietta; Cereda, Cristina; Poletti, Angelo; Alberti, Simon; Carra, Serena
The small heat shock protein B8 (HSPB8) modulates proliferation and migration of breast cancer cells 1-gen-2017 Piccolella, Margherita; Crippa, Valeria; Cristofani, Riccardo; Rusmini, Paola; Galbiati, Mariarita; Cicardi, Maria Elena; Meroni, Marco; Ferri, Nicola; Morelli, FEDERICA FRANCESCA; Carra, Serena; Messi, Elio; Poletti, Angelo
An interaction study in mammalian cells demonstrates weak binding of HSPB2 to BAG3, which is regulated by HSPB3 and abrogated by HSPB8 1-gen-2017 Morelli, FEDERICA FRANCESCA; Mediani, Laura; Heldens, Lonneke; Bertacchini, Jessika; Bigi, Ilaria; Carrà, Arianna Dorotea; Vinet, Jonathan; Carra, Serena
Myopathy associated BAG3 mutations lead to protein aggregation by stalling Hsp70 networks 1-gen-2018 Meister-Broekema, Melanie; Freilich, Rebecca; Jagadeesan, Chandhuru; Rauch, Jennifer N.; Bengoechea, Rocio; Motley, William W.; Kuiper, E. F. Elsiena; Minoia, Melania; Furtado, Gabriel V.; van Waarde, Maria A. W. H.; Bird, Shawn J.; Rebelo, Adriana; Zuchner, Stephan; Pytel, Peter; Scherer, Steven S.; Morelli, Federica F.; Carra, Serena; Weihl, Conrad C.; Bergink, Steven; Gestwicki, Jason E.; Kampinga, Harm H.
Defective ribosomal products challenge nuclear function by impairing nuclear condensate dynamics and immobilizing ubiquitin 1-gen-2019 Mediani, L.; Guillen-Boixet, J.; Vinet, J.; Franzmann, T. M.; Bigi, I.; Mateju, D.; Carra, A. D.; Morelli, F. F.; Pinheiro Tiago, Tatiana Sofia; Poser, I.; Alberti, S.; Carra, S.
Small heat-shock protein HSPB3 promotes myogenesis by regulating the lamin B receptor 1-gen-2021 Tiago, T.; Hummel, B.; Morelli, F. F.; Basile, V.; Vinet, J.; Galli, V.; Mediani, L.; Antoniani, F.; Pomella, S.; Cassandri, M.; Garone, M. G.; Silvestri, B.; Cimino, M.; Cenacchi, G.; Costa, R.; Mouly, V.; Poser, I.; Yeger-Lotem, E.; Rosa, A.; Alberti, S.; Rota, R.; Ben-Zvi, A.; Sawarkar, R.; Carra, S.
Mostrati risultati da 1 a 13 di 13
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